Search on: FACTOR IX, COAGULATION 
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Descriptor English:   Factor IX 
Descriptor Spanish:   Factor IX 
Descriptor Portuguese:   Fator IX 
Synonyms English:   Blood Coagulation Factor IX
Factor 9
Factor IX Complex
Factor IX Fraction
Factor Nine
Factor IX, Coagulation
Christmas Factor
Plasma Thromboplastin Component
Autoprothrombin II
Coagulation Factor IX  
Tree Number:   D08.622.355
D12.776.124.125.375
D23.119.375
Definition English:   Storage-stable blood coagulation factor acting in the intrinsic pathway of blood coagulation. Its activated form, IXa, forms a complex with factor VIII and calcium on platelet factor 3 to activate factor X to Xa. Deficiency of factor IX results in HEMOPHILIA B (Christmas Disease). 
Entry Combination - descr/qualif English:   Factor IX/deficiency use Hemophilia B
 
See Related English:   Coagulants
 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AG agonists AN analysis
AI antagonists & inhibitors BI biosynthesis
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
SE secretion ST standards
SD supply & distribution TU therapeutic use
TO toxicity UL ultrastructure
UR urine  
Record Number:   22169 
Unique Identifier:   D005164 

Occurrence in VHL:
 

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